Odontogenic keratocysts in Nevoid basal cell carcinoma syndrome: a case report
نویسندگان
چکیده
منابع مشابه
Odontogenic keratocysts in Nevoid basal cell carcinoma syndrome: a case report
Nevoid basal cell carcinoma syndrome, a rare autosomal dominant disorder, comprises a number of abnormalities such as multiple nevoid basal cell carcinomas, skeletal abnormalities and multiple odontogenic keratocysts. Considering the rarity of this syndrome, we present a 12-year-old boy affected by this syndrome. He had multiple okcs, calcification of falx cerebri, bifid ribs, frontal bossing a...
متن کاملOdontogenic keratocysts in a 5-year-old: initial manifestations of nevoid basal cell carcinoma syndrome.
The purpose of this paper is to report the occurrence of odontogenic keratocysts in a young child. Odontogenic keratocysts are one of the principal features of nevoid basal cell carcinoma syndrome. Their occurrence in this syndrome is usually during the second or third decades of life. This report describes the occurrence of odontogenic keratocysts in a 5-year-old, which proved to be the initia...
متن کاملnevoid basal cell carcinoma syndrome: a case report
nevoid basal cell carcinoma syndrome (bcns) is an autosomal dominant inherited disorder. multiple organ systems may be affected in this syndrome including abnormalities of the skin, skeletal system, genitourinary system and central nevus system. in this report, we present a case of nevoid basal cell carcinoma syndrome in a 26-year-old male patient. the patient had multiple odontogenic keratocys...
متن کاملOdontogenic keratocysts in nevoid basal cell syndrome (Gorlin’s Syndrome). CT and MR evaluation
Introduction: The nevoid basal cell syndrome (Gorlin’s Syndrome) is a dominant autosomic disorder, characterized by multiple basal cell carcinomas, odontegenic keratocysts, dural calcifications, bone and face malformations, tumors including meduloblastoma and ovaric fibromas, as well as different degrees of mental retardation. Characteristic imagine findings of the Gorlin’s Syndrome are odontog...
متن کاملNevoid Basal Cell Carcinoma Syndrome: Report from the Zurich Nevoid Basal Cell Carcinoma Syndrome Cohort.
BACKGROUND Nevoid basal cell carcinoma syndrome (NBCCS, Gorlin-Goltz syndrome) presents various symptoms and can disfigure patients. The estimated prevalence is around 1:100,000. OBJECTIVE To systematically investigate the clinical manifestations of NBCCS patients of the Zurich register and compare them with those described in 4 epidemiological studies performed in other countries. METHODS ...
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ژورنال
عنوان ژورنال: Cases Journal
سال: 2009
ISSN: 1757-1626
DOI: 10.1186/1757-1626-2-9399